MODERN SURGICAL CORRECTION OF PULMONARY ARTERY ATRESIA WITH MAJOR AORTO-PULMONARY COLLATERAL ARTERIES AND INTERVENTRICULAR DEFECT IN CHILDREN

Abstract

A case of successful treatment of a six-year-old girl with a complex congenital heart disease, rare at this age. The observation shows that atresia of the lungs with a defect in the ventricular septum and large aortopulmonary arteries is a complex group of diseases and requires phased unifocalization and complete recovery in infancy. Since the blood flow to the lungs is completely dependent on these arteries, at a later age in children with the natural course of this complex heart disease, the results are unpredictable. However, since this heart disease is associated with more than 60% mortality by 10 years of age, the authors proposed a change in approach: unifocalization of the pulmonary artery into the right ventricle as the first stage of the procedure. Thus, avoiding complications, timely determining adequate treatment tactics, improving the quality of life.